Item no. |
E-AB-19223-20 |
Manufacturer |
Elabscience
|
Amount |
20uL |
Category |
|
Type |
Antibody Polyclonal |
Applications |
IHC, ELISA |
Specific against |
Human, Mouse |
Host |
Rabbit |
Isotype |
IgG |
ECLASS 10.1 |
32160702 |
ECLASS 11.0 |
32160702 |
UNSPSC |
12352203 |
Alias |
Alpha L iduronate sulfate sulfatase, Alpha-L-iduronate sulfate sulfatase, AW214631, Ids, IDS, Iduronate 2 sulfatase 14 kDa chain, Iduronate 2 sulfatase 42 kDa chain, Iduronate 2 sulfatase, Iduronate 2-sulfatase 14 kDa chain, Iduronate sulfatase, Idursulfa |
Similar products |
IDS, MPS2, SIDS, Alpha L iduronate sulfate sulfatase, Alpha-L-iduronate sulfate sulfatase, AW214631, Ids, Iduronate 2 sulfatase 14 kDa chain, Iduronate 2 sulfatase 42 kDa chain, Iduronate 2 sulfatase, Iduronate 2-sulfatase 14 kDa chain, Iduronate sulfatase, Idursulfase, RP23-29M4.1 |
Available |
|
Research Areas |
Cell Biology |
Synonyms |
Alpha L iduronate sulfate sulfatase, Alpha-L-iduronate sulfate sulfatase, AW214631, Ids, IDS, Iduronate 2 sulfatase 14 kDa chain, Iduronate 2 sulfatase 42 kDa chain, Iduronate 2 sulfatase, Iduronate 2-sulfatase 14 kDa chain, Iduronate sulfatase, Idursulfase, MPS2, RP23-29M4.1, SIDS |
Swissprot |
P22304 |
Background |
Iduronate 2-sulfatase (IDS) is required for the lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations causing IDS deficiency in humans result in the lysosomal storage of these glycosaminoglycans and Hunter syndrome, an X chromosome-linked disease. An internal proteolytic cleavage occurs to produce the mature IDS present in human liver shown to contain a 42 kDa polypeptide N-terminal to a 14 kDa polypeptide.. |
Concentration |
1.02 mg/mL |
Storage |
Store at -20C. Avoid freeze / thaw cycles. |
Immunogen |
Fusion protein of human IDS |
Buffer |
PBS with 0.05% NaN3 and 40% Glycerol, pH7.4 |
Purification Method |
Antigen affinity purification |
Dilution |
IHC 1:50-1:200, ELISA 1:5000-1:10000 |
Conjugation |
Unconjugated |
Gene Accession |
BC006170 |
Note: The presented information and documents (Manual, Product Datasheet, Safety Datasheet and Certificate of Analysis) correspond to our latest update and should serve for orientational purpose only. We do not guarantee the topicality. We would kindly ask you to make a request for specific requirements, if necessary.
All products are intended for research use only (RUO). Not for human, veterinary or therapeutic use.