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GAA ELISA Kit (Mouse) (OKEH04148)

GAA ELISA Kit (Mouse) (OKEH04148)

Item no.	OKEH04148
Manufacturer	AVIVA Systems Biology
Amount	96 Wells
Category	ELISA ELISA & Immunoassays ELISA Kits Immunoassay
Type	Elisa-Kit
Specific against	other
ECLASS 10.1	32160605
ECLASS 11.0	32160605
UNSPSC	41116126
Available
Gene symbol	GAA
Protein name	lysosomal alpha-glucosidase
Protein size	953
Molecular weight	106 kDa
Gene id	14387
Reconstitution and storage	Store as indicated in product manual.
Description of target	This gene encodes a lysosomal acid glucosidase that is involved in the degradation of glycogen. The encoded preproprotein undergoes proteolytic processing to generate a mature enzyme that cleaves alpha-1-4 and alpha-1-6 glycosidic bonds of glycogen, maltose and intermediate oligosaccharides within the lysosome. Mice lacking the encoded protein exhibit symptoms similar to human Pompe syndrome such as accumulation of glycogen in cardiac and skeletal muscle lysosomes resulting in reduced mobility and strength. Alternative splicing of this gene results in multiple transcript variants.
Assay info	Assay Methodology: Quantitative Sandwich ELISA
Sensitivity	0.4 ng/mL
Drywet	Wet Ice

Note: The presented information and documents (Manual, Product Datasheet, Safety Datasheet and Certificate of Analysis) correspond to our latest update and should serve for orientational purpose only. We do not guarantee the topicality. We would kindly ask you to make a request for specific requirements, if necessary.

All products are intended for research use only (RUO). Not for human, veterinary or therapeutic use.

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Amount: 96 Wells

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Delivery expected until 9/13/2024

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